WebRight atrial isomerism (RAI) is a severe complex congenital heart defect resulting from embryonic disruption of proper left-right axis determination. RAI is usually characterized … Webisomerism翻譯:異構現象。了解更多。 Other persons may have discordance between the thoracic organs, which are usually arranged, and the abdominal organs, which are mirror-imaged, but no evidence of isomerism.
Asplenia with cardiovascular anomalies - Wikipedia
WebJan 3, 2024 · Our objective was to review our experience with isomerism associated with univentricular hearts and evaluate the prevalence of pulmonary versus systemic outflow obstruction. We identified those prenatally or postnatally diagnosed, between September 2004 and October 2024, with right and left isomerism and a functionally univentricular … WebN2 - Background: Twin AV nodes and resulting supraventricular tachycardia (SVT) have been described in right atrial isomerism (RAI). Objective: We sought to analyze the long-term outcome of patients with RAI with a focus on rhythm disturbances. bar aura
Right atrial isomerism - NIH Genetic Testing Registry (GTR) - NCBI
WebOct 4, 2024 · Right atrial appendage isomerism — Right atrial appendage isomerism, also referred to as right atrial isomerism (RAI), results in two right sides with bilateral right … WebCommon atrium (40-80%). Septum primum and secundum are commonly absent, and both atrial appendages exhibit morphologic features of the right atrium (bilateral extension of the pectinate muscles). Bilateral superior venae cavae (40-70%) with unroofed coronary sinus (30-100%). Dual sinus nodes are common. WebPatients with heterotaxy syndrome, especially those with right atrial isomerism (RAI), have frequently been found to have congenital anomalies of the conduction system. Twin atrioventricular (AV) nodes (TAVN) may exist in association with an unbalanced common AV canal and they may be connected via a sling of conduction tissue, first described ... bar aurora barzago